Pityriasis Rubra Pilaris - Symptoms & Treatment
Pityriasis rubra pilaris (PRP) is a chronic papulosquamous disorder of unidentified etiology described by reddish orange peeling plaques, palmoplantar keratoderma, along with keratotic follicular papules. The disease may growth to erythroderma with diverse areas of uninvolved skin, the so-called islands of sparing. Pityriasis rubra pilaris is not in fact a single condition, but rather a faction of unusual eruptions that cause red scaly patches containing dry plugged pores. It may wrap the entire body, or just the elbows and knees. PRP generally affects adults over 40, but some children are also affected. The familial form of pityriasis rubra pilaris usually initiate in early childhood and has an autosomal leading inheritance pattern.
Pityriasis rubra pilaris is the name given to a cluster of rare skin disorders that present with reddish-orange coloured scaling patches with well defined borders. The disease may concern entire body or just restrict to some parts for instance the elbows and knees, palms and soles. It is generally accompanied by eminent erythematous spots (papules) on the skin. The papules are the most vital diagnostic feature, being more or less acuminate, reddish brown, about pinhead size, and topped by a central horny plug. Diagnosis is by clinical look and may be supported by biopsy. Discrepancy diagnosis includes seborrheic dermatitis (in children) and psoriasis when disease arises on the scalp, elbows, and knees. Treatment is extremely intricate and empiric.
Causes of Pityriasis rubra pilaris
Some causes & risk factors of Pityriasis rubra pilaris are as follows:
- Pityriasis rubra pilaris is usually sporadic, but in several forms it may be partially hereditary.
- Fungal infection may too be a cause of the disease.
Symptoms of Pityriasis rubra pilaris
The possible symptoms of Pityriasis rubra pilaris includes:
- Reddish-orange areas on the skin.
- Painful itching.
- Thickening of the coat on the feet and hands.
- Lesions of the face.
- Inflammation of the legs, feet and other parts of the body.
Treatments of Pityriasis rubra pilaris
The value of treatment is not easy to evaluate, as the clinical course is so variable for each of the different types of Pityriasis rubra pilaris. In general, the hereditary forms of PRP tend to persist throughout life whilst the sporadically acquired forms tend to resolve spontaneously ultimately. The greatest treatment is Accutane or Soriatane pills. These are strictly associated "retinoid" medications. Topical corticosteroids may afford some patient soothe, but they are believed to have little long-term therapeutic effect. Emollients decrease fissuring and dryness, providing some patient relieve. Petroleum jelly or various proprietary emollients may be used.